The Acquired Metabolic Disorders of the Nervous System, Hepatic Stupor and Coma (Hepatic, or Portal-Systemic Encephalopathy)
Adams & Victors Principles of Neurology Chp 40, pg 1142, Ropper, A.H.,et al, 2014
Clinicopathologic Conference, Noncirrhotic hyperammonemia after Roux-en-Y Gastric Bypass
NEJM 389:1221-1230, Case 30-2023, 2023
Chemotherapy-Associated Hyperammonemic Encephalopathy
Neurol 94:e874-e877, Briard, J.N.,et al, 2020
Pathophysiology and Management of Hyperammonemia in Organ Transplant Patients
Am J Kidney Dis PMID:31040091, Seethapathy, H. & Fenves, A.Z., 2019
Idiopathic Hyperammonemia after Solid Organ Transplantation: Primarily a Lung Problem? A Single-Center Experience and Systematic Review
ClinTransplant 31:e12957, Krutsinger, D.,et al, 2017
Clinicopathologic Conference, Fulminant Liver Failure Associated with Hepatitis B Virus Infection
NEJM 375:163-171, Case 21-2016, 2016
A 27-Year Old Man with Rapidly Progressive Coma
Neurol 85:e74-e78, Wong,J.M.,et al, 2015
Risk Factors of Hyperammonemia in Patients with Epilepsy Under Valproic Acid Therapy
Medicine 93:e66, Tseng, Y.L.,et al, 2014
Inherited Metabolic Diseases of the Nervous System, Inherited Hypeammonemia
Adams & Victors Principles of Neurology, Chp 37, pg 952, Ropper, A.H.,et al, 2014
Diffusion-Weighted Imaging in Acute Hyperammonemic Encephalopathy
Neurohosp 3:125-130, Rosario, M.,et al, 2013
Hyperammonemic Encephalopathy
Neurol 78:600-601, Capizzano,A.A.,et al, 2012
A Young Man with Progressive Subcortical Lesions and Optic Nerve Atrophy
Neurol 79:e63, Komatsuzaki, S.,et al, 2012
Differential Diagnosis of Bilateral Abnormalities of the Basal Ganglia and Thalamus
RadioGraphics 31:5-30, Hegde,A.N.,et al, 2011
MRI in Methylmalonic Acidemia
Neurol 74:e14, Bindu, P.S.,et al, 2010
Acute Hepatic Encephalopathy: Diffusion-Weighted and Fluid-Attenuated Inversion Recovery Findings, and Correlation With Plasma Ammonia Level and Clinical Outcome
AJNR 31:1471-1479, McKinney,A.M.,et al, 2010
Acute Hyperammonemic Encephalopathy in Adults: Imaging Findings
AJNR 32:413-418, U-King-Im,J.M.,et al, 2010
MRI Findings Associated With Acute Liver Failure
Neurol 72:2130-2131, Fridman,V.,et al, 2009
Mysteriod Episodic Coma
Lancet 371:2222, Ferenczi,E.,et al., 2008
MR Imaging Findings in Hepatic Encephalopathy
AJNR 29:1612-1621, Rovira,A.,et al, 2008
Brain MR Imaging in Acute Hyperammonemic Encephalopathy Arising from Late-Onset Ornithine Transcarbamylase Deficiency
AJNR 24:390-393, Takanashi,J-i.,et al, 2003
Hyperammonemic Encephalopathy in Multiple Myeloma
NEJM 346:1674-1675, Kwan,L.,et al, 2002
Urinary Tract Infection and Coma
Lancet 360:996, De Jonghe,B.,et al, 2002
Coma in a Young Anorexic Woman
Lancet 357:1944, Blans,M.J.,et al, 2001
Acute Hepatic Encephalopathy with Diffuse Cortical Lesions
Neuroradiology 43:551-554, Arnold, S.M.,et al, 2001
Valproate-Induced Hyperammonemic Encephalopathy in the Presence of Topiramate
Neurol 54:230-232, Hamer,H.M.,et al, 2000
Clumsiness, Confusion, Coma, and Valproate
Lancet 353:1408, Ellaway,C.J.,et al, 1999
Treatment of Hepatic Encephalopathy
NEJM 337:473-479, Riordan,S.M.,et al, 1997
Hepatic Encephalopathy and Ascites
Lancet 350:1309-1315, Jalan,R.&Hayes,P.C., 1997
Inborn Errors of Urea Synthesis
Ann Neurol 35:133-141, Batshaw,M.L., 1994
Postpartum Coma and Death Due to Carbamoyl-Phosphate Synthetase I Deficiency
Ann Int Med 120:216-217, Wong,L-J.C.,et al, 1994
Valproic Acid-Induced Hyperammonemic Encephalopathy:MR Appearance
AJNR 15:1779-1781, Baganz,M.D.&Dross,P.E., 1994
Ornithine Transcarbamylase Deficiency Presenting with Strokelike Episodes
J Pediatrics 122:423-425, Christodoulou,J.,et al, 1993
Arginase Deficiency Presenting as Cerebral Palsy
Pediatrics 91:995-996, Scheuerle,A.E.,et al, 1993
MRI Pallidal Hyperintensity & Brain Atrophy in Cirrhotic Pts:2 Different MRI Patterns of Clin Deterior?
Neurol 43:2570-2573, Kulisevsky,J.,et al, 1993
Clinicopath Conf
Hepatic Encephalopathy in a 40-Year-Old Woman, Am J Med 90:374-3801991., , 1991
Hyperammonemia in Women with a Mutation at the Ornithine Carbamoyltransferase Locus
NEJM 322:1652-1669, Arn,P.H.,et al, 1990
Hyperammonemic Encephalopathy in Urinary Diversion with Urea-Splitting Urinary Tract Infection
Arch Int Med 150:2389-2392, Kaveggia,F.F.,et al, 1990
Episodic Confusion and Tremor Associated with Extrahepatic Portacaval Shunting in Cirrhotic Liver Disease
Neurol 39:403-405, Russell,D.M.,et al, 1989
Reye's Syndrome in Adults, Diagnostic Considerations
Arch Int Med 147:61-64, Meythaler,J.M.&Varma,R.R., 1987
Hepatic Encephalopathy
NEJM 313:865-873, Fraser,C.L.&Arieff,A.I., 1985
Neurologic Outcome in Children with Inborn Errors of Urea Synthesis
NEJM 310:1500-1505, Msall,M.,et al, 1984
Treatment of Episodic Hyperammonemia in Children with Inborn Errors of Urea Synthesis
NEJM 310:1630-1634, Brushlow,S.W.,et al, 1984
Hyperammonemic Encephalopathy Due to Essential Amino Acid Hyperalimentation
Arch Int Med 144:2278-2279, Grazer,R.E.,et al, 1984
Hyperammonemic Encephalopathy Related to Ureterosigmoidostomy
Arch Neurol 41:1211-1212, Edwards,R.H., 1984
Detection of Urea Cycle Enzymopathies in Childhood
Arch Neurol 41:758-760, Trauner,D.A.,et al, 1984
Clinical Features of Carbamyl Phosphate Synthetase-I Deficiency in an Adult
Ann Neurol 16:90-93, Call,G.,et al, 1984
Cerebellar Hemorrhage Complication Methylmalonic & Propionic Acidemia
Arch Neurol 41:1293-1296, Dave,P.,et al, 1984
Hyperammonemic Encephalopathy During Hemodialysis
Ann Int Med 99:190-191, Canzanello,V.J.,et al, 1983
Hyperammonemic Encephalopathy Caused By Infection In A Neurogenic Bladder
NEJM 304:766-768, Drayna,C.J.,et al, 1981